Abstract. Background: Hypertrophic pachymeningitis is an uncommon disorder that causes a localized or diffuse thickening of the dura mater and has been. Summary: Idiopathic hypertrophic cranial pachymeningitis is a rare inflammatory disease with diffused involvement of the dura. Often, the definite diagnosis is. Hypertrophic pachymeningitis is a unique clinical entity characterised by fibrosis and thickening of the duramater with resulting neurological dysfunction.

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No Shinkei Geka ; A year-old lady presented with headache and progressive painless loss of vision in both the eyes over a periods of 6 months. Author information Article notes Copyright and License information Disclaimer.

Dural masses dural masses meningioma grading and histological variants grade I meningothelial meningioma fibrous meningioma microcystic meningioma psammomatous meningioma angiomatous meningioma secretory meningioma metaplastic meningioma cartilaginous meningioma lipomatous meningioma melanotic meningioma myxoid meningioma osseous meningioma xanthomatous meningioma lymphoplasmacyte-rich meningioma grade II clear cell meningioma chordoid meningioma atypical meningioma grade III rhabdoid meningioma papillary meningioma anaplastic meningioma a.

Idiopathic cranial hypertrophic pachymeningitis responsive to antituberculous therapy. Acta Derm Venereol ; Neurology and general medicine. Unable to process the form.

Idiopathic hypertrophic pachymeningitis.

A case of posterior fossa hypertrophic pachymeningitis with hydrocephalus. Tuberculous hypertrophic pachymeningitis involving the posterior fossa and high cervical region. Open access journal indexed with Index Medicus. Can J Neurol Sci ; Long term hpyertrophic of idiopathic hypertrophic cranial pachymeningitis by lymphocytapheresis.


Hypertrophic pachymeningitis

About Blog Go ad-free. Hypertrophic pachymeningitis can be diagnosed with contrast MRI of brain when the clinician maintains a high index of suspicion for this condition.

Pardee I, Knox lC: Published by Wolters Kluwer – Medknow. You can also scroll through stacks with your mouse wheel or the keyboard arrow keys. MR imaging revealed diffuse dural enhancement and thickening, along with left fronto parieto occipital edema.

One case had necrotizing vasculitis of the small arteries located in the dura and the cerebral surface. Support Center Support Center. Neurological complications of sarcoidosis. Hypertrophic pachymeningitis is a rare form of diffuse inflammatory disease that causes thickening of the dura mater.

Rest of the neurological examination was normal. Related Radiopaedia articles Infections of the central nervous system CNS infections classification by etiology viral eastern equine encephalitis enterovirus rhomboencephalitis flavivirus encephalitis Japanese encephalitis West Nile fever Murray Valley encephalitis St.

A study of seven cases.

Four patients underwent biopsy of the dura, and the pathological study showed non-specific inflammatory changes. CT or MR imaging studies should be obtained to identify mass lesions in the brain stem or skull base.


Eur J Radiol ; P-ANCA positive Wegener’s granulomatosis pachymenongitis with hypertrophic pachymeningitis and multiple cranial neuropathies: Cerebrospinal fluid analysis revealed normal cell count, protein and sugar levels.

Best cases from the AFIP: There were no giant cells, caseation necrosis, or epitheloid granuloma. Presence of associated leptomeningeal enhancement or parenchymal abnormalities with the exception of brain edema should suggest an alternate diagnosis.

Idiopathic hypertrophic cranial pachymeningitis.

Idiopathic hypertrophic pachymeningitis.

Ann Indian Acad Neurol. Articles Cases Courses Quiz. A succesful case of hypertrophic pachgmeningitis pachymeningitis treated with optic nerve decompression. Imaging appearance of pachymeningeal tuberculosis.

Cases and figures Imaging differential diagnosis. It was first described by Charcot and later by Naffziger and Stern.

Both the patient’s routine biochemistry was normal, and they were further evaluated to rule hypertfophic secondary causes The serum was negative for rheumatoid factor, antinuclear antibodies. It is a fibrosing inflammatory process that involves the dura mater. Thank you for updating your details.

Inflammatory hypertrophic cranial pachymeningitis. Two patients received surgical intervention. A case of rheumatoid pachymeningitis.